176. Lung function in patients with primary ciliary dyskinesia: an iPCD Cohort study.

Halbeisen FS, Goutaki M, Spycher BD, Amirav I, Behan L, Boon M, Hogg C, Casaulta C, Crowley S, Haarman EG, Karadag B, Koerner-Rettberg C, Loebinger MR, Mazurek H, Morgan L, Nielsen KG, Omran H, Santamaria F, Schwerk N, Thouvenin G, Yiallouros P, Lucas JS, Latzin P, Kuehni CE.
Eur Respir J. 2018 Aug 23;52(2). pii: 1801040. doi: 10.1183/13993003.01040-2018. Print 2018 Aug.
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177. Variability of monthly nitrogen multiple-breath washout during one year in children with cystic fibrosis.
Green K, Kongstad T, Skov M, Buchvald F, Rosthøj S, Marott JL, Gustafsson P, Pressler T, Nielsen KG.
J Cyst Fibros. 2018 Mar;17(2):242-248. doi: 10.1016/j.jcf.2017.11.007. Epub 2017 Dec 19.
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178. The effect of time-of-day and chest physiotherapy on multiple breath washout measures in children with clinically stable cystic fibrosis.
Voldby C, Green K, Rosthøj S, Kongstad T, Philipsen L, Buchvald F, Skov M, Pressler T, Gustafsson P, Nielsen KG.
PLoS One. 2018 Jan 10;13(1):e0190894. doi: 10.1371/journal.pone.0190894. eCollection 2018.
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179. Preschool Multiple-Breath Washout Testing. An Official American Thoracic Society Technical Statement.
Robinson PD, Latzin P, Ramsey KA, Stanojevic S, Aurora P, Davis SD, Gappa M, Hall GL, Horsley A, Jensen R, Lum S, Milla C, Nielsen KG, Pittman JE, Rosenfeld M, Singer F, Subbarao P, Gustafsson PM, Ratjen F; ATS Assembly on Pediatrics.
Am J Respir Crit Care Med. 2018 Mar 1;197(5):e1-e19. doi: 10.1164/rccm.201801-0074ST.
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180. The accessibility of topical treatment in the paranasal sinuses on operated cystic fibrosis patients assessed by scintigraphy.
Aanaes K, Alanin MC, Nielsen KG, Moller Jorgensen M, von Buchwald C, Hoiby N, Johansen HK, Johannesen HH, Mortensen J.
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181. Mutations in C11orf70 Cause Primary Ciliary Dyskinesia with Randomization of Left/Right Body Asymmetry Due to Defects of Outer and Inner Dynein Arms.
Höben IM, Hjeij R, Olbrich H, Dougherty GW, Nöthe-Menchen T, Aprea I, Frank D, Pennekamp P, Dworniczak B, Wallmeier J, Raidt J, Nielsen KG, Philipsen MC, Santamaria F, Venditto L, Amirav I, Mussaffi H, Prenzel F, Wu K, Bakey Z, Schmidts M, Loges NT, Omran H.
Am J Hum Genet. 2018 May 3;102(5):973-984. doi: 10.1016/j.ajhg.2018.03.025.
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182. Initiating transitional care for adolescents with cystic fibrosis at the age of 12 is both feasible and promising.
Skov M, Teilmann G, Damgaard IN, Nielsen KG, Hertz PG, Holgersen MG, Presfeldt M, Dalager AMS, Brask M, Boisen KA.
Acta Paediatr. 2018 Nov;107(11):1977-1982. doi: 10.1111/apa.14388. Epub 2018 May 29.
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183. Associations of physical activity with childhood asthma, a population study based on the WHO - health behaviour in school-aged children survey.
Lochte L, Petersen PE, Nielsen KG, Andersen A, Platts-Mills TAE.
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184. Infant nasal nitric oxide over time: natural evolution and impact of respiratory tract infection.
Marthin JK, Philipsen MC, Rosthoj S, Nielsen KG.
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185. Fitness and lung function in children with primary ciliary dyskinesia and cystic fibrosis.
Ring AM, Buchvald FF, Holgersen MG, Green K, Nielsen KG.
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186. Ventilation inhomogeneity and NO and CO diffusing capacity in ex-premature school children.
Sørensen JK, Buchvald F, Berg AK, Robinson PD, Nielsen KG.
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187. Variation in treatment strategies for the eradication of Pseudomonas aeruginosa in primary ciliary dyskinesia across European centers.
Crowley S, Holgersen MG, Nielsen KG.
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188. The increased purchase of asthma medication for individuals born preterm seems to wane with age: A register-based longitudinal national cohort study.
Damgaard ALB, Gregersen R, Lange T, Buchvald F, Hansen BM, Greisen G.
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189. Antibody response against Mycobacterium avium complex in cystic fibrosis patients measured by a novel IgG ELISA test.
Ravnholt C, Qvist T, Kolpen M, Pressler T, Skov M, Høiby N.
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190. The importance of early diagnosis of Mycobacterium abscessus complex in patients with cystic fibrosis.
Ravnholt C, Kolpen M, Skov M, Moser C, Katzenstein TL, Pressler T, Høiby N, Qvist T.
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16. 191. Osteoporosis Is Associated with Deteriorating Clinical Status in Adults with Cystic Fibrosis.
Mathiesen IH, Pressler T, Oturai P, Katzenstein TL, Skov M, Frikke-Schmidt R, Hitz MF.
Int J Endocrinol. 2018 Mar 26;2018:4803974. doi: 10.1155/2018/4803974. eCollection 2018.
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192. Living with cystic fibrosis - a qualitative study of a life coaching intervention.
Knudsen KB, Boisen KA, Katzenstein TL, Mortensen LH, Pressler T, Skov M, Jarden M.
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193. Seasonal fluctuation of lung function in cystic fibrosis: A national register-based study in two northern European populations.
Qvist T, Schlüter DK, Rajabzadeh V, Diggle PJ, Pressler T, Carr SB, Taylor-Robinson D.
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19. 194. Impact of cystic fibrosis on birthweight: a population based study of children in Denmark and Wales.
Schlüter DK, Griffiths R, Adam A, Akbari A, Heaven ML, Paranjothy S, Nybo Andersen AM, Carr SB, Pressler T, Diggle PJ, Taylor-Robinson D.
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20. 195. The choice of lung function reference equation affects clinical trial eligibility: Results from a cystic fibrosis cohort.
Mathiesen IH, Ronit A, Pressler T.
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21. 196. Aquagenic wrinkling of the palms in patients with cystic fibrosis.
Kaiser H, Brustad N, Pressler T, Bygum A.
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197. Prevalence and characteristics of chronic kidney disease among Danish adults with cystic fibrosis.
Berg KH, Ryom L, Faurholt-Jepsen D, Pressler T, Katzenstein TL.
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198. Proceedings of the 3rd BEAT-PCD Conference and 4th PCD Training School
Hannah Farley, Bruna Rubbo, Zuzanna Bukowy-Bieryllo, Mahmoud Fassad, Myrofora Goutaki, Katharine Harman, Claire Hogg, Claudia E. Kuehni, Susana Lopes, Kim G. Nielsen, Dominic P. Norris, Ana Reula, Nisreen Rumman, Amelia Shoemark, Hannah Wilkins, Agatha Wisse, Jane S. Lucas and June K. Marthin.

BMC Proceedings 2018 12 (Suppl 16) :64


160.  Qvist T, Pressler T, Katzenstein TL, Høiby N, Collins MT. Evaluation of a bovine antibody test for diagnosing Mycobacterium avium complex in patients with cystic fibrosis. Pediatr Pulmonol. 2017 Jan;52(1):34-40. doi: 10.1002/ppul.23608.


161. Alanin MC, Aanaes K, Høiby N, Pressler T, Skov M, Nielsen KG, Johansen HK, von Buchwald C.

Sinus surgery can improve quality of life, lung infections, and lung function in patients with primary ciliary dyskinesia

Int Forum Allergy Rhinol. 2017 Mar;7(3):240-247. doi: 10.1002/alr.21873. Epub 2016 Nov 23.


162. Waldmann, E., D. Taylor-Robinson, N. Klein, T. Kneib, T. Pressler, M. Schmid and A. Mayr (2017). "Boosting joint models for longitudinal and time-to-event data." Biom J.  2017 Mar 21. doi: 10.1002/bimj.201600158. [Epub ahead of print]


163. Marthin JK, Stevens EM, Larsen LA, Christensen ST, Nielsen KG.

Patient-specific three-dimensional explant spheroids derived from human nasal airway epithelium: a simple methodological approach for ex vivo studies of primary ciliary dyskinesia.

Cilia. 2017 Mar 23;6:3. doi: 10.1186/s13630-017-0049-5. eCollection 2017.


164. Høiby N, Bjarnsholt T, Moser C, Jensen PØ, Kolpen M, Qvist T, Aanaes K, Pressler T, Skov M, Ciofu O.

Diagnosis of biofilm infections in cystic fibrosis patients.

APMIS. 2017 Apr;125(4):339-343. doi: 10.1111/apm.12689. Review.


165. Kongstad TGreen KBuchvald FSkov MPressler TNielsen KG. Association between spirometry controlled chest CT scores using computer-animated biofeedback and clinical markers of lung disease in children with cystic fibrosis. Eur Clin Respir J. 2017 May 2;4(1):1318027. doi: 10.1080/20018525.2017.1318027. eCollection 2017.


166. Knudsen KB, Pressler T, Mortensen LH, Jarden M, Skov M, Quittner AL, Katzenstein T, Boisen KA.

Erratum to: Associations between adherence, depressive symptoms and health-related quality of life in young adults with cystic fibrosis.

Springerplus. 2017 May 31;5(1):2119. doi: 10.1186/s40064-017-3789-1. eCollection 2016.


167. Kongstad T, Green K, Buchvald F, Skov M, Pressler T, Nielsen KG.

Association between spirometry controlled chest CT scores using computer-animated biofeedback and clinical markers of lung disease in children with cystic fibrosis.

Eur Clin Respir J. 2017 May 2;4(1):1318027. doi: 10.1080/20018525.2017.1318027. eCollection 2017.

. doi: 10.1016/j.jhin.2017.04.020. Epub 2017 Apr 27.


168. Ratjen, F., C. Hug, G. Marigowda, S. Tian, X. Huang, S. Stanojevic, C. E. Milla, P. D. Robinson, D. Waltz and J. C. Davies (2017). "Efficacy and safety of lumacaftor and ivacaftor in patients aged 6-11 years with cystic fibrosis homozygous for F508del-CFTR: a randomised, placebo-controlled phase 3 trial." Lancet Respir Med. Jun 8. pii: S2213-2600(17)30215-1. doi: 10.1016/S2213-2600(17)30215-1. [Epub ahead of print]


169. Knudsen KB, Pressler T, Mortensen LH, Jarden M, Boisen KA, Skov M, Quittner AL, Katzenstein TL.

Coach to cope: feasibility of a life coaching program for young adults with cystic fibrosis.

Patient Prefer Adherence. 2017 Sep 21;11:1613-1623. doi: 10.2147/PPA.S141267. eCollection 2017.


170. Fernández-Barat L, Ciofu O, Kragh KN, Pressler T, Johansen U, Motos A, Torres A, Hoiby N. Phenotypic shift in Pseudomonas aeruginosa populations from cystic fibrosis lungs after 2-week antipseudomonal treatment. J Cyst Fibros. 2016 Sep 16. pii: S1569-1993(16)30601-4. doi: 10.1016/j.jcf.2016.08.005. [Epub ahead of print] PubMed PMID: 27651273.


171. Bregnballe V, Boisen KA, Schiotz PO, Pressler T, Lomborg K.

Flying the nest: a challenge for young adults with cystic fibrosis and their parents. Patient Prefer Adherence. 2017;11:229-36.


172. Ronit A, Mathiesen IH, Gelpi M, Benfield T, Gerstoft J, Pressler T, et al.

Small airway dysfunction in well-treated never-smoking HIV-infected individuals. Eur Respir J. 2017;49(3).


173. Schultz AN, Hoiby N, Nielsen XC, Pressler T, Dalhoff K, Duno M, et al.

Individual pharmacokinetic variation leads to underdosing of ciprofloxacin in some cystic fibrosis patients. Pediatr Pulmonol. 2017;52(3):319-23.

174. Hoiby, N., T. Bjarnsholt, C. Moser, P. O. Jensen, M. Kolpen, T. Qvist, K. Aanaes, T. Pressler, M. Skov and O. Ciofu (2017).

"Diagnosis of biofilm infections in cystic fibrosis patients." APMIS 125(4): 339-343.

175. Ronit, A., M. Gelpi, J. Argentiero, I. Mathiesen, S. D. Nielsen, T. Pressler and A. L. Quittner (2017). "Electronic applications for the CFQ-R scoring." Respir Res 18(1): 108.


Buchvald F, Phillipsen LD, Hjuler T, Nielsen KG.
Pediatr Pulmonol. 2016 Nov;51(11):1200-1205. doi: 10.1002/ppul.23530.
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Alanin MC, Aanaes K, Høiby N, Pressler T, Skov M, Nielsen KG, Johansen HK, von Buchwald C.
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Loomba RS, Danduran M, Nielsen KG, Ring AM, Kovach J, Anderson RH.
Pediatr Cardiol. 2016 Nov 23. [Epub ahead of print]
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Ioan I, Demoulin-Alexikova S, Coutier L, Bonabel C, Kirkby J, Nielsen KG, Tomalak W, Thompson B, Schweitzer C, Robinson PD, Marchal F.
Eur Respir J. 2016 Dec;48(6):1804-1807. doi: 10.1183/13993003.01302-2016. No abstract available. 
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Kobbernagel HE, Buchvald FF, Haarman EG, Casaulta C, Collins SA, Hogg C, Kuehni CE, Lucas JS, Omran H, Quittner AL, Werner C, Nielsen KG.
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Sommer LM, Alanin MC, Marvig RL, Nielsen KG, Høiby N, von Buchwald C, Molin S, Johansen HK.
Sci Rep. 2016 Jun 28;6:28732. doi: 10.1038/srep28732.
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Alanin MC, Aanaes K, Høiby N, Pressler T, Skov M, Nielsen KG, Taylor-Robinson D, Waldmann E, Krogh Johansen H, von Buchwald C.
Rhinology. 2016 Sep;54(3):206-13. doi: 10.4193/Rhin15.347.
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Lochte L, Nielsen KG, Petersen PE, Platts-Mills TA.
BMC Pediatr. 2016 Apr 18;16:50. doi: 10.1186/s12887-016-0571-4. Review.
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Sisman Y, Buchvald F, Blyme AK, Mortensen J, Nielsen KG.
Pediatr Pulmonol. 2016 Aug;51(8):830-7. doi: 10.1002/ppul.23360.
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Werner C, Lablans M, Ataian M, Raidt J, Wallmeier J, Große-Onnebrink J, Kuehni CE, Haarman EG, Leigh MW, Quittner AL, Lucas JS, Hogg C, Witt M, Priftis KN, Yiallouros P, Nielsen KG, Santamaria F, Ückert F, Omran H.
Eur Respir J. 2016 Mar;47(3):849-59. doi: 10.1183/13993003.00776-2015.
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Green K, Ejlertsen JS, Madsen A, Buchvald FF, Kongstad T, Kobbernagel H, Gustafsson PM, Nielsen KG.
Pediatr Pulmonol. 2016 Jun;51(6):624-32. doi: 10.1002/ppul.23339.
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Kristensen KH, Rytter MJ, Sørensen AC, Christensen VB, Namusoke H, Skov M, Andreassen BU, Friis H.
Ugeskr Laeger. 2016 Oct 3;178(40). pii: V03160185. Danish.

Knudsen KB, Pressler T, Mortensen LH, Jarden M, Skov M, Quittner AL, Katzenstein T, Boisen KA.
Springerplus. 2016 Jul 29;5(1):1216. doi: 10.1186/s40064-016-2862-5.

155. Lea M. Sommer, Rasmus L. Marvig, Adela Luján, Anna Koza, Tacjana Pressler, Søren Molin1, and Helle K. Johansen. Is genotyping of single isolates sufficient for population structure analysis of Pseudomonas aeruginosa in cystic fibrosis airways? BMC Genomics201617:589. DOI: 10.1186/s12864-016-2873-1

156. Knudsen KB, Pressler T, Mortensen LH, Jarden M, Skov M, Quittner AL, Katzenstein T, Boisen KA. Associations between adherence, depressive symptoms and health-related quality of life in young adults with cystic fibrosis. Springerplus. 2016 Jul 29;5(1):1216. doi: 10.1186/s40064-016-2862-5. PubMed PMID: 27516954; PubMed Central PMCID: PMC4967055.

157. Qvist T, Pressler T, Katzenstein TL, Høiby N, Collins MT. Evaluation of a bovine antibody test for diagnosing Mycobacterium avium complex in patients with cystic fibrosis. Pediatr Pulmonol. 2016 Sep 20. doi: 10.1002/ppul.23608. [Epub ahead of print] PubMed PMID: 27648735.

158. Fernández-Barat L, Ciofu O, Kragh KN, Pressler T, Johansen U, Motos A, Torres A, Hoiby N. Phenotypic shift in Pseudomonas aeruginosa populations from cystic fibrosis lungs after 2-week antipseudomonal treatment. J Cyst Fibros. 2016 Sep 16. pii: S1569-1993(16)30601-4. doi: 10.1016/j.jcf.2016.08.005. [Epub ahead of print] PubMed PMID: 27651273. 

159. Bryant JM, Grogono DM, Rodriguez-Rincon D, Everall I, Brown KP, Moreno P, Verma D, Hill E, Drijkoningen J, Gilligan P, Esther CR, Noone PG, Giddings O, Bell SC, Thomson R, Wainwright CE, Coulter C, Pandey S, Wood ME, Stockwell RE, Ramsay KA, Sherrard LJ, Kidd TJ, Jabbour N, Johnson GR, Knibbs LD, Morawska L, Sly PD, Jones A, Bilton D, Laurenson I, Ruddy M, Bourke S, Bowler IC, Chapman SJ, Clayton A, Cullen M, Dempsey O, Denton M, Desai M, Drew RJ, Edenborough F, Evans J, Folb J, Daniels T, Humphrey H, Isalska B, Jensen-Fangel S, Jönsson B, Jones AM, Katzenstein TL, Lillebaek T, MacGregor G, Mayell S, Millar M, Modha D, Nash EF, O'Brien C, O'Brien D, Ohri C, Pao CS, Peckham D, Perrin F, Perry A, Pressler T, Prtak L, Qvist T, Robb A, Rodgers H, Schaffer K, Shafi N, van Ingen J, Walshaw M, Watson D, West N, Whitehouse J, Haworth CS, Harris SR, Ordway D, Parkhill J, Floto RA. Emergence and spread of a human-transmissible multidrug-resistant nontuberculous mycobacterium. Science. 2016 Nov 11;354(6313):751-757. PubMed PMID: 27846606; PubMed Central PMCID: PMC5142603.


136. Frommer A, Hjeij R, Loges NT, Edelbusch C, Jahnke C, Raidt J, Werner C, Wallmeier J, Große-Onnebrink J, Olbrich H, Cindrić S, Jaspers M, Boon M, Memari Y, Durbin R, Kolb-Kokocinski A, Sauer S, Marthin JK, Nielsen KG, Amirav I, Elias N, Eitan K, Shoseyov D, Haeffner K, Omran H.

Immunofluorescence Analysis and Diagnosis of Primary Ciliary Dyskinesia with Radial Spoke Defects.

Am J Respir Cell Mol Biol. 2015 Mar 19. [Epub ahead of print]

37. Hansen C, Skov M.

Evidence for the efficacy of aztreonam for inhalation solution in the management of Pseudomonas aeruginosa in patients with cystic fibrosis.

Ther Adv Respir Dis. 2015 Feb;9(1):16-21.

138. Mathias Munkholm, Kim Gjerum Nielsen & Jann Mortensen

Clinical value of measurement of pulmonary radioaerosol mucociliary clearance in the work up of primary ciliary dyskinesia

12/2015; 5(1):118. DOI:10.1186/s13550-015-0118-y​​

139. Paul D Robinson · Janet Stocks·Francois Marchal · Kim G Nielsen · Bruce R Thompson · Waldemar Tomalak · Jane Kirkby

Poor standardisation of plethysmographic specific airways resistance measurement despite widespread use.

European Respiratory Journal 08/2015; DOI:10.1183/13993003.00377-2015 · 7.13 Impact Factor ​

140. Heike Olbrich · Carolin Cremers · Niki T Loges · Claudius Werner · Kim G Nielsen · June K Marthin · Maria Philipsen · Julia Wallmeier · Petra Pennekamp · Tabea Menchen · Christine Edelbusch · Gerard W Dougherty · Oliver Schwartz · Holger Thiele · Janine Altmüller · Frank Rommelmann · Heymut Omran

Loss-of-Function GAS8 Mutations Cause Primary Ciliary Dyskinesia and Disrupt the Nexin-Dynein Regulatory Complex.

The American Journal of Human Genetics 09/2015; DOI:10.1016/j.ajhg.2015.08.012 · 10.93 Impact Factor

141. Damgaard AL, Hansen BM, Mathiasen R, Buchvald F, Lange T, Greisen G.

Prematurity and prescription asthma medication from childhood to young adulthood: a Danish national cohort study.

PLoS One. 2015 Feb 4;10(2):e0117253. doi: 10.1371/journal.pone.0117253. eCollection 2015.


120. Skov M, Pressler T, Lykkesfeldt J, Poulsen HE, Jensen PØ, Johansen HK, Qvist T, Kræmer D, Høiby N, Ciofu O.

The effect of short-term, high-dose oral N-acetylcysteine treatment on oxidative stress markers in cystic fibrosis patients with chronic P. aeruginosa infection - A pilot study.

J Cyst Fibros. 2015 Mar;14(2):211-8. doi: 10.1016/j.jcf.2014.09.015. Epub 2014 Oct 23.


121. Qvist T, Gilljam M, Jönsson B, Taylor-Robinson D, Jensen-Fangel S, Wang M, Svahn A, Kötz K, Hansson L, Hollsing A, Hansen CR, Finstad PL, Pressler T, Høiby N, Katzenstein TL; Scandinavian Cystic Fibrosis Study Consortium (SCFSC).

Epidemiology of nontuberculous mycobacteria among patients with cystic fibrosis in Scandinavia.
J Cyst Fibros. 2015 Jan;14(1):46-52. doi: 10.1016/j.jcf.2014.08.002. Epub 2014 Aug 30.


122. Uhlving HH, Andersen CB, Christensen IJ, Gormsen M, Pedersen KD, Buchvald F, Heilmann C, Nielsen KG, Mortensen J, Moser C, Sengeløv H, Müller KG.

Biopsy-verified bronchiolitis obliterans and other noninfectious lung pathologies after allogeneic hematopoietic stem cell transplantation.

Biol Blood Marrow Transplant. 2015 Mar;21(3):531-8. doi: 10.1016/j.bbmt.2014.12.004. Epub 2014 Dec 9.


123. Alanin MC, Johansen HK, Aanaes K, Høiby N, Pressler T, Skov M, Nielsen KG, von Buchwald C.

Simultaneous sinus and lung infections in patients with primary ciliary dyskinesia.

Acta Otolaryngol. 2015 Jan;135(1):58-63. doi: 10.3109/00016489.2014.962185. Epub 2014 Nov 5.


124. Qvist T, Gilljam M, Jönsson B, Taylor-Robinson D, Jensen-Fangel S, Wang M, Svahn A, Kötz K, Hansson L, Hollsing A, Hansen CR, Finstad PL, Pressler T, Høiby N, Katzenstein TL;

Epidemiology of nontuberculous mycobacteria among patients with cystic fibrosis in Scandinavia.

Scandinavian Cystic Fibrosis Study Consortium (SCFSC).

J Cyst Fibros. 2015 Jan;14(1):46-52. doi: 10.1016/j.jcf.2014.08.002. Epub 2014 Aug 30.


125. Knudsen KB, Mathiesen ER, Eriksen V, Skov M, Nielsen KG, Johannesen J, Pressler T The development of diabetes among Danish cystic fibrosis patients over the last two decades.

Pediatr Diabetes. 2015 May;16(3):219-26. doi: 10.1111/pedi.12143. Epub 2014 Jun 1.


126. Joensen O, Paff T, Haarman EG, Skovgaard IM, Jensen PØ, Bjarnsholt T, Nielsen KG.

Exhaled breath analysis using electronic nose in cystic fibrosis and primary ciliary dyskinesia patients with chronic pulmonary infections.

PLoS One. 2014 Dec 26;9(12):e115584. doi: 10.1371/journal.pone.0115584. eCollection 2014.


127. Uhlving HH, Mathiesen S, Buchvald F, Green K, Heilmann C, Gustafsson P, Müller K, Nielsen KG.

Small airways dysfunction in long-term survivors of pediatric stem cell transplantation.

Pediatr Pulmonol. 2014 May 21. doi: 10.1002/ppul.23058. [Epub ahead of print]


128. Thomas A, Hanel B, Marott JL, Buchvald F, Mortensen J, Nielsen KG.

The single-breath diffusing capacity of CO and NO in healthy children of European descent.

PLoS One. 2014 Dec 16;9(12):e113177. doi: 10.1371/journal.pone.0113177. eCollection 2014.


129. Buchvald F, Nielsen KG.

 Diffuse lung disease in children.

Ugeskr Laeger. 2014 Aug 18;176(34). pii: V05130316. Danish.


130. Hjeij R, Onoufriadis A, Watson CM, Slagle CE, Klena NT, Dougherty GW, Kurkowiak M, Loges NT, Diggle CP, Morante NF, Gabriel GC, Lemke KL, Li Y, Pennekamp P, Menchen T, Konert F, Marthin JK, Mans DA, Letteboer SJ, Werner C, Burgoyne T, Westermann C, Rutman A, Carr IM, O'Callaghan C, Moya E, Chung EM; UK10K Consortium, Sheridan E, Nielsen KG, Roepman R, Bartscherer K, Burdine RD, Lo CW, Omran H, Mitchison HM.

CCDC151 mutations cause primary ciliary dyskinesia by disruption of the outer dynein arm docking complex formation.

Am J Hum Genet. 2014 Sep 4;95(3):257-74. doi: 10.1016/j.ajhg.2014.08.005.


131. Mathiesen S, Uhlving HH, Buchvald F, Hanel B, Nielsen KG, Müller K.

 Aerobic exercise capacity at long-term follow-up after paediatric allogeneic haematopoietic SCT.

Bone Marrow Transplant. 2014 Nov;49(11):1393-9. doi: 10.1038/bmt.2014.172. Epub 2014 Aug 11.


132. Maglione M, Bush A, Nielsen KG, Hogg C, Montella S, Marthin JK, Di Giorgio A, Santamaria F.

Multicenter analysis of body mass index, lung function, and sputum microbiology in primary ciliary dyskinesia.

Pediatr Pulmonol. 2014 Dec;49(12):1243-50. doi: 10.1002/ppul.22984. Epub 2014 Jan 13.

133. Mathiesen PR, Buchvald F, Nielsen KG, Herlin T, Friis T, Nielsen S.

Pulmonary function and autoantibodies in a long-term follow-up of juvenile dermatomyositis patients.

Rheumatology (Oxford). 2014 Apr;53 (4):644-9. doi: 10.1093/rheumatology/ket380. Epub 2013 Dec 5.​ 

134. Aanaes K, Eickhardt S, Johansen HK, von Buchwald C, Skov M, Høiby N, Bjarnsholt T.

Sinus biofilms in patients with cystic fibrosis: is adjusted eradication therapy needed?

Eur Arch Otorhinolaryngol. 2014 Oct 9. [Epub ahead of print]

135. Lewis AE, Høi-Hansen CE, Buchvald F, Petersen W.

Idiopathic pulmonary haemosiderosis in a one-year-old girl with Down syndrome.

Ugeskr Laeger. 2014 Sep 22;176(39). pii: V04140253. Danish.


101.Qvist T, Pressler T, Thomsen VO, Skov M, Iversen M, Katzenstein TL.
Nontuberculous Mycobacterial Disease Is Not a Contraindication to Lung Transplantation in Patients With Cystic Fibrosis: A Retrospective Analysis in a Danish Patient Population.
Transplant Proc.2013;45:342-5

102. Aanaes K, Johansen HK, Poulsen SS, Pressler T, Buchwald C, Høiby N.
"Secretory IgA as a diagnostic tool for Pseudomonas aeruginosa respiratory colonization."
J Cyst Fibros. 2013;12:81-87.

103.Christina Schjellerup Dalbøge, Tacjana Pressler, Niels Høiby, Kim Gjerum Nielsen, Helle Krogh Johansen
.A COHORT STUDY of the Copenhagen CF centre Eradication Strategy against Staphylococcus aureus in
 patients with CF.
J Cyst Fibros. 2013;12:42-8

104.Aanaes K, von Buchwald C, Hjuler T, Skov M, Alanin M, Johansen HK.
The effect of sinus surgery with intensive follow-up on pathogenic sinus bacteria in patients with cystic fibrosis.
Am J Rhinol Allergy. 2013 Jan;27(1):e1-4.

105. Yu D, Buchvald F, Brandt B, Nielsen KG.
Seventeen-year study shows rise in parapneumonic infections with higher treatment failure after chest tube drainage.
Acta Paediatr. 2013 Sep 30.

106. Christensen PM, Maltbæk N, Jørgensen IM, Nielsen KG.
Can flow-volume loops be used to diagnose exercise induced laryngeal obstructions? A comparison study examining the accuracy and inter-rater agreement of flow volume loops as a diagnostic tool.
Prim Care Respir J. 2013 Sep;22(3):306-11.

107. Aanaes K, Johansen HK, Skov M, Buchvald FF, Hjuler T, Pressler T, Hoiby N, Nielsen KG,
von Buchwald C.
Clinical effects of sinus surgery and adjuvant therapy in cystic fibrosis patients - can chronic
lung infections be postponed?
Rhinology. 2013 Sep;51(3):222-30.

108. Moore DJ, Onoufriadis A, Shoemark A, Simpson MA, Zur Lage PI, de Castro SC, Bartoloni L,
Gallone G, Petridi S, Woollard WJ, Antony D, Schmidts M, Didonna T, Makrythanasis P, Bevillard J,
Mongan NP, Djakow J, Pals G, Lucas JS, Marthin JK, Nielsen KG, Santoni F, Guipponi M, Hogg C,
Antonarakis SE, Emes RD, Chung EM, Greene ND, Blouin JL, Jarman AP, Mitchison HM
Mutations in ZMYND10, a Gene Essential for Proper Axonemal Assembly of Inner and Outer Dynein Arms in Humans and Flies, Cause Primary Ciliary Dyskinesia.
Am J Hum Genet. 2013 Aug 8;93(2):346-56.

109. Kobbernagel HE, Nielsen KG, Hanel B.
Hypoxic challenge test applied to healthy
children: influence of body positions and exertion
on pulse oximetric saturation.
Arch Dis Child. 2013 Aug;98(8):602-6.

110. Uhlving HH, Bang CL, Christensen IJ, Buchvald F, Nielsen KG, Heilmann CJ, Müller KG.
Lung function after allogeneic hematopoietic stem cell transplantation in children: a longitudinal study in a population-based cohort.
Biol Blood Marrow Transplant. 2013 Sep;19(9):1348-54.

111. Rosenfeld M, Allen J, Arets BH, Aurora P, Beydon N, Calogero C, Castile RG, Davis SD, Fuchs S, Gappa M, Gustaffson PM, Hall GL, Jones MH, Kirkby JC, Kraemer R, Lombardi E, Lum S, Mayer OH, Merkus P, Nielsen KG, Oliver C, Oostveen E, Ranganathan S, Ren CL, Robinson PD, Seddon PC, Sly PD, Sockrider MM, Sonnappa S, Stocks J, Subbarao P, Tepper RS, Vilozni D; American Thoracic Society Assembly on Pediatrics Working Group on Infant and Preschool Lung Function Testing.
An official American Thoracic Society workshop report: optimal lung function tests for monitoring cystic fibrosis, bronchopulmonary dysplasia, and recurrent wheezing in children less than 6 years of age.
Ann Am Thorac Soc. 2013 Apr;10(2):S1-S11.

112. Idorn L, Hanel B, Jensen AS, Juul K, Reimers JI, Nielsen KG, Søndergaard L.
New insights into the aspects of pulmonary diffusing capacity in Fontan patients.
Cardiol Young. 2013 Apr 3:1-9

113. Borgwardt L, Dali CI, Fogh J, Månsson JE, Olsen KJ, Beck HC, Nielsen KG, Nielsen LH, Olsen SO, Riise Stensland HM, Nilssen O, Wibrand F, Thuesen AM, Pearl T, Haugsted U, Saftig P, Blanz J, Jones SA, Tylki-Szymanska A, Guffon-Fouiloux N, Beck M, Lund AM.
Enzyme replacement therapy for alpha-mannosidosis: 12 months follow-up of a single centre, randomised, multiple dose study.
J Inherit Metab Dis. 2013 Nov;36(6):1015-24.

114. Marthin JK, Nielsen KG.
Hand-held tidal breathing nasal nitric oxide measurement--a promising targeted case-finding tool for the diagnosis of primary ciliary dyskinesia.
PLoS One. 2013;8(2):e57262.

115. Idorn L, Juul K, Jensen AS, Hanel B, Nielsen KG, Andersen H, Reimers JI, Sørensen KE, Søndergaard L.
Arrhythmia and exercise intolerance in Fontan patients: current status and future burden.
Int J Cardiol. 2013 Sep 30;168(2):1458-65.
116. Yu D, Buchvald F, Brandt B, Nielsen KG.
Seventeen-year study shows rise in parapneumonic infections with higher treatment failure after chest tube drainage.
Acta Paediatr. 2013 Sep 30.

117. Madsen A, Green K, Buchvald F, Hanel B, Nielsen KG.
Aerobic fitness in children and young adults with primary ciliary dyskinesia.
PLoS One. 2013 Aug 19;8(8):e71409.

118. Kongstad T, Buchvald FF, Green K, Lindblad A, Robinson TE, Nielsen KG.
Improved air trapping evaluation in chest computed tomography in children with cystic fibrosis using real-time spirometric monitoring and biofeedback.
J Cyst Fibros. 2013 Dec;12(6):559-66.

119. Pernille M. Christensen, John-Helge Heimdal, Kent L. Christopher, Caterina Bucca, Giovanna Cantarella, Gerhard Friedrich, Thomas Halvorsen, Felix Herth, Harald Jung, Michael J. Morris, Marc Remacle, Niels Rasmussen, and Janet A. Wilson.
ERS/ELS/ACCP 2013 international consensus conference nomenclature on inducible laryngeal obstructions.
Eur Respir Rev 2015; 24: 445–450


86. Uhlving HH, Buchvald F, Heilmann CJ, Kim Gjerum Nielsen,Gormsen M, Müller KG.
Bronchiolitis obliterans after allo-SCT: clinical criteria and treatment options.
Bone Marrow Transplant. 2012;47: 1020-9

87. Jacob Rasmussen, Kasper Aanæs, Rikke Norling, Kim Gjerum Nielsen, Helle Krogh Johansen, Christian von Buchwald.
CT of the paranasal sinuses is not a valid indicator for sinus surgery in CF patients.
J Cyst Fibros. 2012;11:93-9

88.Kongstad T, Buchvald F, Brenøe J, Petersen BL, Tabor A, Kim Gjerum Nielsen.
Radiology, histology and short-term outcome of asymptomatic congenital thoracic malformations.
Acta Paediatr. 2012;101:155-8.

89.Jacob Rasmussen, Aanæs K, Norling R, Kim Gjerum Nielsen, Johansen HK, von Buchwald C.
CT of the paranasal sinuses is not a valid indicator for sinus surgery in CF patients.
J Cyst Fibros. 2012;11:93-9.

90.Helle Krogh Johansen, Kasper Aanaes,
Tania Pressler, Kim Gjerum Nielsen,
Jacob Fisker,
Marianne Skov, Niels Høiby, Christian von Buchwald.
Colonisation and infection of the paranasal
sinuses in cystic fibrosis patients is
accompanied by a reduced PMN response.
J Cyst Fibros. 2012;11:525-31.

91.Heike Olbrich, Miriam Schmidts, Claudius Werner, Alexandros Onoufriadis, Niki T. Loges, Johanna Raidt,
Nora Fanni Banki, Amelia Shoemark, Tom Burgoyne, Saeed Al Turki, Matthew E. Hurles, UK10K, Gabriele Köhler, Josef Schroeder, Gudrun Nürnberg, Peter Nürnberg, Eddie M. K. Chung, Richard Reinhardt, June K. Marthin, Kim Gjerum Nielsen, Hannah M. Mitchison, and Heymut Omran.
Recessive HYDIN mutations cause Primary Ciliary Dyskinesia without randomization of left/right body asymmetry.
Am J Hum Genet. 2012;91:672-84.

92.Chawes BL, Jensen T, Olsen R, Joensen F, Nielsen KG, Buchvald F.
Plastic bronchitis in a ten year-old boy with Fontan circulation.
Ugeskr Laeger. 2012;174:1674-5.

93.Green K, Buchvald FF, Marthin JK, Hanel B, Gustafsson PM, Nielsen KG.
Ventilation inhomogeneity in children with primary ciliary dyskinesia.
Thorax. 2012;67:49-53.

94.Arendrup MC, Jensen RH, Grif K, Skov M, Pressler T, Johansen HK, Lass-FlörlC.
In vivo emergence of Aspergillus terreus with reduced azole susceptibility and a cyp51a M217I alteration.
J Infect Dis. 2012;206:981-5.

95.Johansen HK, Aanaes K, Pressler T, Nielsen KG, Fisker J, Skov M, Høiby N, von Buchwald C.
Colonisation and infection of the paranasal sinuses in cystic fibrosis patients is accompaniedby a reduced PMN response.
J Cyst Fibros. 2012;11:525-31.

96. Taylor-Robinson D, Whitehead M, Diderichsen F, Olesen HV, Pressler T, Smyth RL, Diggle P.
"Understanding the natural progression in %FEV1 decline in patients with cystic fibrosis:a longitudinal study."
Thorax. 2012 ;67:860-63

97.Assael BM, Pressler T, Bilton D, Fayon M, Fischer R, Chiron R, Larosa M, Knoop C, McElvaney N, Lewis SA, Bresnik M, Montgomery AB, Oermann CM; For the AZLI Active Comparator Study Group.
Inhaled aztreonamlysine vs. inhaled tobramycin in cystic fibrosis: A comparativeefficacy trial.
J Cyst Fibros. 2012 Sep 14.

98.Aanaes K, Rasmussen N, Pressler T, Segelmark M, Johansen HK, Lindberg U, Høiby N, Carlsson M, Wieslander J, von Buchwald C. 
Extensiveendoscopic image-guided sinus surgery decreases BPIANCA in patients with cystic fibrosis.
Scand J Immunol. 2012;76:573-9.

99.Maiken C. Arendrup, Rasmus H. Jensen, Katharina Grif, Marianne Skov, Tacjana Pressler, Helle K. Johansen, and Cornelia Lass-Flörl
In VivoEmergence of Aspergillus terreus with Reduced Azole Susceptibility anda 
Cyp51a M217I Alteration.
J Infect Dis. 2012; 15;206:981-5.

100.Döring G, Flume P, Heijerman H, Elborn JS; Consensus Study Group.
Treatment of lung infection in patients with cystic fibrosis: current and future strategies.
J Cyst Fibros. 2012;11:461-79​


73. T. Pincikova, K. Nilsson, I. E. Moen, G. Fluge, A. Hollsing, P. K. Knudsen, A. Lindblad, L. Mared, T. Pressler, L. Hjelte..
Vitamin D deficiency as a risk factor for cystic fibrosis-related diabetes in the Scandinavian Cystic Fibrosis Nutritional Study.
Diabetologia. 2011.

74.Pincikova T, Nilsson K, Moen IE, Karpati F, Fluge G, Hollsing A, Knudsen PK, Lindblad A, Mared L, Pressler T, Hjelte L; Scandinavian Cystic Fibrosis Study Consortium.
Inverse relation between vitamin D and serum total immunoglobulin G in the Scandinavian Cystic Fibrosis Nutritional Study.
Eur J Clin Nutr. 2011;65:102-9.

75. Marthin JK, Kim Gjerum Nielsen.
Choice of Nasal Nitric Oxide Technique as first Line Test for Primary Ciliary Dyskinesia.
Eur Respir J. 2011 Mar;37(3):559-65.

76. Dalbøge CS, Hansen CR, Pressler T, Høiby N, Johansen HK.
Chronic pulmonary infection with Stenotrophomonas maltophilia and lung function in patients with cystic fibrosis.
J Cyst Fibros. 2011;10:318-25.

77. Pressler T, Bohmova C, Conway S, Dumcius S, Hjelte L, Høiby N, Kollberg H, Tümmler B, Vavrova V.
Chronic Pseudomonas aeruginosa infection definition: EuroCareCF Working Group report.
J Cyst Fibros. 2011;10 Suppl 2:S75-8.

78. Pressler, T.
Targeting Airway Inflammation in Cystic fibrosis in Children: Past, Present, and Future.
Pediatric Drugs:June 2011;13:141-7

79. Inger Elisabeth Moen, Kristina Nilsson, Anna Andersson, Morten Wang Fagerland, Gjermund Fluge, Annika Ericsson Hollsing, Marita Gilljam, Lena Mared, Tacjana Pressler, Henriette Santi, Olav-Trond Storrøsten, Lena Hjelte.
Dietary intake and nutritional status in a Scandinavian adult cystic fibrosis-population compared with recommendations.
Food & Nutrition Research 2011, 55

80. Mortensen KL, Jensen RH, Johansen HK, Skov M, Pressler T, Howard SJ, Leatherbarrow H, Mellado E, Arendrup MC.
Aspergillus species and other molds in respiratory samples from patients with cystic fibrosis: a laboratory-based study with focus on Aspergillus fumigatus azole resistance.
J Clin Microbiol. 2011;49:2243-51.

81. Aanaes K, Rickelt LF, Johansen HK, von Buchwald C, Pressler T, Høiby N, Jensen PØ.
Decreased mucosal oxygen tension in the maxillary sinuses in patients with cystic fibrosis.
J Cyst Fibros, 2011. 10: p. 114-20.

82. Becker-Heck A. Zohn IE, Okabe N, Pollck, Lanhart KB, Sullivan- Brown J, McSheen J, Loges NT, Olbrich H, Haeffner K, Fliegauf M, Horvarth J, Reinhardt B, Nielsen KG, Marthin JK, Baktai G, Anderson KV, Geisler B, Niswander L, Omran H, Burdine RD.
The coiled-coil domain containing protein CCDC40 is essential for motile cilia function and left-right axis formation.
Nature Genet. 2011;43:79-84.

83. Merveille AC, Davis EE, Becker-Heck A, Legendre M,Amirav I, Bataille G, Belmont J, beydon N, Billen F, Clement A, Clercx C, Coste A, Crosbie R, de Blic J, Deleuze S, Duquesnoy P, Escalier D, Escudier E, Fliegauf M, Horvath J, Hill K, Jorissen M, Just J, Kispert A, lathrop M, Loges NT, Marthin JK, Momozawa Y, Nielsen KG, Plbrich H, Papon JF, Rayet I,Roger G, Schmidts M, Tenreiro H, Towbin JA, Zelenika D, Zentgraf H, Georges M,
Lequarre AS, Katsanis N, Omran H, mselem S,. 
CCDC39 is required for assembly of inner dynein arms and the dynein regulatory complex and for normal ciliary motility in humans and dogs.
Nature Genet. 2011;43:72-78.

84. Mette Siemsen, Niels E O Andersen, Kim Gjerum Nielsen.
EBUS in a 6 year old boy with enlarged hilar lymph nodes.
Journal of Bronchology and Interventional Pulmonology 2011,18:205.

85. Frederik Buchvald, LA Kristensen, Bodil Laub Petersen, Karen Damgaard, Robin Deterding, MD; Claire Langston, MD, Leland L Fan, MD; Gail H Deutsch, MD; Megan K Dishop, Kim Gjerum Nielsen.
Frequency, Treatment and Functional Outcome in Children with Hypersensitivity Pneumonitis.
Pediatr Pulmonol. 2011;46:1098-107.​


63. Chawes BL, Buchvald F, Bischoff AL, Loland L, Hermansen M, Halkjaer LB, Bønnelykke K, Bisgaard H.
Elevated exhaled nitric oxide in high-risk neonates precedes transient early but not persistent wheeze.
Am J Respir Crit Care Med. 2010;182:138-42.

64. Rafiq S, Meldgaard CW, Buchvald F, Brandt B.
[Congenital aplasia of left-sided pericardium].
Ugeskr Laeger. 2010;172:547-8. Danish.

65. Raaschou-Nielsen O, Hermansen MN, Loland L, Buchvald F, Pipper CB, Sørensen M, Loft S, Bisgaard H.
Long-term exposure to indoor air pollution and wheezing symptoms in infants.
Indoor Air. 2010;20:159-67.

66. Hansen CR, Pressler T, Jensen PO, Bjarnsholt T, Høiby N.
Inflammation in Achromobacter xylosoxidans infected cystic fibrosis patients.
J Cyst Fibrosis. 2010;9:51-58.

67. Marthin JK, Petersen N, Skovgaard LT. Kim Gjerum Nielsen.
Lung Function in Patients with Primary Ciliary Dyskinesia. A Cross Sectional and Three-decade Longitudinal Study.
Am J Respir Crit Care Med.1;181:1262-8.

68. Kirkby J, Stanojevic S, Lum S, Bardier M, Beatdsmore C, Custovic A, Nielsen KG, Paton J, Tomalak W,Stocks J.
Reference equations for specific airway resistance in children: the asthma UK initiative.
Eur Respir J. 2010;36:622-9.

69. Kuehni CE, Frischer T, Strippoli MP, Maurer E, Bush A, Kim Gjerum Nielsen,  Escribano A, Lucas JS, Yiallouros P, Omran H, Eber E, O'Callaghan C, Snijders D, Barbato A;
For the ERS task force on primary ciliary dyskinesia in children. Factors influencing age at diagnosis of primary ciliary dyskinesia in European children.
Eur Respir J. 2010, 36:1248-58.

70. Nørskov-Lauritsen N, Johansen HK, Fenger MG, Nielsen XC, Pressler T, Olesen HV, Høiby N. H.K. Johansen, M.G. Fenger, 
Unusual Distribution of Burkholderia cepacia Complex Species in Danish Cystic Fibrosis Clinics May Stem from Restricted transmission between Patients.
J Clin Microbiol, 2010;48:2981-3.

71. Andersen JB, Mortensen J, Damgaard K, Skov M, Sparup J, Petersen BL, Rechnitzer C, Borgwardt L.
Fourteen-year-old girl with endobronchial carcinoid tumour presenting with asthma and lobar emphysema.
Clin Respir j. 2010, 4:120-4.

72. Olesen HV, Pressler T, Hjelte L, Mared L, Lindblad A, Knudsen PK, Laerum BN, Johannesson M;
Gender differences in the Scandinavian cystic fibrosis population.
Pediatr Pulmonol. 2010: 45: pp 959-965.​


55. Kolpen M, Hansen CR, Bjarnsholt T, Moser C, Christensen LD, van Gennip M, Ciofu O, Mandsberg L,
Kharazmi A, Döring G, Givskov M, Høiby N, Jensen PØ.
Polymorphonuclear leucocytes consume oxygen in sputum from chronic Pseudomonas aeruginosa pneumonia in cystic fibrosis.
Thorax, 2009. 65: p. 57-62.

56. Knudsen PK, Olesen HV, Høiby N, Johannesson M, Karpati F, Laerum BN, Meyer P, Pressler T, Lindblad A; Scandinavian CF Study Consortium (SCFSC). 
Differences in prevalence and treatment of Pseudomonas aeruginosa in cystic fibrosis centres in Denmark, Norway and Sweden.
J Cyst Fibros, 2009. 8.135-42

57. Pressler T, Karpati F, Granström M, Knudsen PK, Lindblad A, Hjelte L, Olesen HV, Meyer P, Høiby N;
Scandinavian CF Study Consortium.
Diagnostic significance of measurements of specific IgG antibodies to Pseudomonas aeruginosa by three different serological methods.
Journal of cystic fibrosis. 2009. 8: 37-42.

58. Hansen CR, Pressler T, Hoiby N, Johansen HK.
Long-term, low-dose azithromycin treatment reduces the incidence but increases macrolide resistance in Staphylococcus aureus in Danish CF patients.
Journal of cystic fibrosis. 2009. 8: 58-62.

59. Fluge G, Olesen HV, Gilljam M, Meyer P, Pressler T, Storrösten OT, Karpati F, Hjelte L.
Co-morbidity of cystic fibrosis and celiac disease in Scandinavian cystic fibrosis patients.
J Cyst Fibros., 2009. 8: p. 198-202.

60. Bjarnsholt T, Jensen PØ, Fiandaca MJ, Pedersen J, Hansen CR, Andersen CB, Pressler T, Givskov M, Høiby N.
Pseudomonas aeruginosa biofilms in the respiratory tract of cystic fibrosis patients.
Pediatr Pulmonol., 2009. 44: p. 547-58.

61. Heijerman H, Westerman E, Conway S, Touw D, Döring G; consensus working group.
Inhaled medication and inhalation devices for lung disease in patients with cystic fibrosis: A European consensus.
J Cyst Fibros., 2009. 8: p. 295-315.

62. Barbato A., T. Frischer, C. E. Kuehni, D. Snijders, I. Azevedo, G. Baktai, L. Bartoloni, E. Eber, A. Escribano, E. Haarman, B. Hesselmar, C. Hogg, M. Jorissen, J. Lucas, Kim Gjerum Nielsen, C. O'Callaghan, H. Omran, P. Pohunek, M-P. F. Strippoli, and A. Bush.
Primary ciliary dyskinesia: a consensus statement on diagnostic and treatment approaches in children.
Eur Respir J 2009;34 1264-1276.


51. Birgitte Boysen Kjaer, Jorgen Skov Jensen, Kim Gjerum Nielsen, Anders Fomsgaard, Blenda Böttiger, Birthe Dohn, and Hans Bisgaard. 
Lung function and bronchial responsiveness after Mycoplasma pneumonie infection in early childhood.
Pediatr Pulmonol. 2008;43:567-75.

52. Johansen HK, Moskowitz SM, Ciofu O, Pressler T, Høiby N.,
Spread of colistin resistant non-mucoid Pseudomonas aeruginosa among chronically infected Danish cystic fibrosis patients.
J Cyst Fibros., 2008. 7: 391-7.

53. Hansen, C.R., T. Pressler, and N. Hoiby,
Early aggressive eradication therapy for intermittent Pseudomonas aeruginosa airway colonization in cystic fibrosis patients: 15 years experience.
J Cyst Fibros., 2008. 7: 523-30.

54. Pressler, T.,
Review of recombinant human deoxyribonuclease (rhDNase) in the management of patients with cystic fibrosis.
Biologics: Targets & Therapy, 2008. 2. 611-7.


47. Carlsson M., Eriksson L., Pressler T., Kornfalt R., Mared L., Meyer P., et al.,
Autoantibody response to BPI predict disease severity and outcome in cystic fibrosis.
J Cyst Fibros. 2007, 6: 228-33.

48. Jensen P.O., Bjarnsholt T., Phipps R., Rasmussen T.B., Calum H., Christoffersen L, et al.,
Rapid necrotic killing of polymorphonuclear leukocytes is caused by quorum-sensingcontrolled production of rhamnolipid by Pseudomonas aeruginosa.
Microbiology. 2007, 153: 1329-38.

49. June K. Marthin, Jann Mortensen, Tacjana Pressler, Kim Gjerum Nielsen.
Pulmonary Radioaerosol Mucociliary Clearance in Diagnosis of Primary Ciliary Dyskinesia.
Chest.2007; 132: 966-976.

50. Bisgaard H, Hermansen MN, Buchvald F, Loland L, Halkjaer LB, Bønnelykke K, Brasholt M, Heltberg A, Vissing NH, Thorsen SV, Stage M, Pipper CB.
Childhood asthma after bacterial colonization of the airway in neonates.
N Engl J Med. 2007;357:1487-95.


36. Halkjaer LB, Loland L, Buchvald FF, Agner T, Skov L, Strand M, Bisgaard H.
Development of atopic dermatitis during the first 3 years of life: the Copenhagen prospective study on asthma in childhood cohort study in high-risk children.
Arch Dermatol. 2006;142:561-6.

37. Bisgaard H, Hermansen MN, Loland L, Halkjaer LB, Buchvald F.
Intermittent inhaled corticosteroids in infants with episodic wheezing.
N Engl J Med. 2006 11;354:1998-2005.

38. Loland L, Buchvald FF, Halkjaer LB, Anhøj J, Hall GL, Persson T, Krause TG, Bisgaard H.
Sensitivity of bronchial responsiveness measurements in young infants.
Chest. 2006;129:669-75.

39. Kim Gjerum Nielsen.
Lung function and bronchial responsiveness in young children.
Thesis in Dan Med Bull.2006; 53: 46-75.

40. Mette Hermansen, Kim Gjerum Nielsen, Frederik Buchvald, Jakob Jessing Jespersen, Thomas Bengtsson, Hans Bisgaard.
Acute Relief of Exercise-Induced Bronchoconstriction by Inhaled Formoterol in Children With Persistent Asthma.
Chest 2006; 129:1203–1209.

41. Kim Gjerum Nielsen. P
Plethysmographic specific airway resistance.
Paediatr Respir Rev. 2006; 7: suppl 1: 17-19.

42. Kim Gjerum Nielsen.
Forced oscillation technique.
Paediatr Respir Rev. 2006; 7: suppl 1: 8-10.

43. Pressler T., Frederiksen B., Skov M., Garred P., Koch C., Høiby N.
Early rise of anti-pseudomonas antibodies and a mucoid phenotype of Pseudomonas aeruginosa are risk factors for development of chronic lung infection. A case control study.
J Cyst Fibros. 2006, 5: 9-15.

44. Rønne Hansen C., Pressler T., Høiby N., Gormsen M.
Chronic infection with Achromobacter xylosoxidans in cystic fibrosis patients; a retrospective case control study.
J Cyst Fibros. 2006,5: 245-51.

45. Frederiksen B., Pressler T., Hansen A., Koch C., Høiby N.
Effect of aerosolized rhDNase (Pulmozyme) on pulmonary colonization in patients with cystic fibrosis.
Acta Paediatr. 2006, 95: 1070-4.

46. Andersen H.U., Lanng S., Pressler T., Laugesen C.S., Mathiesen E.R.
Cystic fibrosisrelated diabetes: the presence of microvascular diabetes complications.
Diabetes Care. 2006, 29: 2660-3.


24. Bundgaard H, Skov M.
Hypokaleamia-induced arrhytmia – the assassin in beta-2 agonist treated patients?
Letter in BMJ 2005.

25. Skov M, McKay K, Koch C, Cooper PJ.
Prevalence of allergic broncho-pulmonary aspergillosis in cystic fibrosis in an area with a high frequency of atopy.
Resp Medicine 2005; 99: 887-893.

26. Oana Ciofu, Bente Riis, Tacjana Pressler, Henrik Enghusen Poulsen and Niels Høiby.
Occurrence of Hypermutable Pseudomonas aeruginosa in Cystic Fibrosis Patients is associated with the Oxidative Stress Caused by Chronic Lung Inflammation.
Antimicrobial Agents and Chemotherapy. 2005, 49: 2276-2282.

27. Christopher M. Burton, Tacjana Pressler, Nils Milman.
Pulmonary sarcoidosis in a Child with Cystic Fibrosis. Pediatric pulmonology.
Pediatr Pulmonol. 2005, 39: 473-7.

28. Christine Rønne Hansen, Tacjana Pressler, Christian Koch and Niels Høiby.
Longterm Azitromycin treatment of cystic fibrosis patients with chronic P. aeruginosa infection.
J Cyst Fibros. 2005, 4: 35-40.

29. Moser, C. Jensen P.O., Pressler T., Frederiksen B., Lanng S., Kharazmi A., Koch C., Høiby N.
Serum concentrations of GM-CSF and G-CSF correlate with the Th1/Th2 cytokine response in cystic fibrosis patients with chronic Pseudomonas aeruginosa lung infection.
Apmis, 2005. 113: p. 400-9.

30. Høiby N., Frederiksen B., Pressler T., et al.,
Eradication of earlyPseudomonas aeruginosa infection in cystic fibrosis patients with chronic Pseudomonas aeruginosa lung infection.
J Cyst Fibros, 2005. 4 (Suppl 2): p. 49-54.

31. Kim Gjerum Nielsen, H Bisgaard.
Hyperventilation with Cold versus Dry Air in 2 – to 5 –year-old Children with Asthma.
Am J Respir Crit Care Med 2005; 171: 238-241.

32. Hans Bisgaard, Kim Gjerum Nielsen. P
Plethysmographic Measurements of Specific Airway Resistance in Young Children.
Chest 2005; 128: 355-362.

33. Frederik Buchvald, Mette Hermansen, Kim Gjerum Nielsen, Hans Bisgaard.
Exhaled Nitric Oxide Predicts Exercise Induced Bronchoconstriction in Asthmatic School Children.
Chest 2005; 128:1964–1967.

34. Kim Gjerum Nielsen, Bisgaard H.
Cold air challenge and specific airway resistance in preschool children.
Paediatr Respir Rev. 2005;6:255-66.

35. Buchvald F, Baraldi E, Carraro S, Gaston B, De Jongste J,Pijnenburg MW, Silkoff PE, Bisgaard H.
Measurements of exhaled nitric oxide in healthy subjects age 4 to 17 years.
 J Allergy Clin Immunol. 2005;115:1130-6.​


17. D Jeganathan, R Chodhari, M Meeks, O Færoe, D Smyth, Kim Gjerum Nielsen, A S. Luder, I Amirav, H Bisgaard, R M Gardiner, E M K Chung, H M Mitchison.
Loci for primary ciliary dyskinesia map to chromosome 16p12.1-12.2 and 15q13.1-15.1 in Faroe Islands and Israeli Druze genetic isolates.
J Med Genet 2004; 41:233-240.

18. Kim Gjerum Nielsen, T Pressler, B Klug, C Koch, H Bisgaard.
Serial Lung Function and Responsiveness in Cystic Fibrosis during Early Childhood.
Am J Respir Crit Care Med 2004; 169: 1209-1216.

19. Johansen H.K., Norregaard L., Gotzsche P.C., Pressler T., Koch C., Høiby N.
Antibody response to Pseudomonas aeruginosa in cystic fibrosis patients: A marker of therapeutic success? A 30-year Cohort study of survival in Danish CF patients after onset of chronic P. aeruginosa lung infection.
Pediatr Pulmonol. 2004, 37: 427-32.

20. Bo Bech, Tanja Pressler, Martin Iversen, Jørn Carlsen, Nils Milman, Kirsten Eliasen, Mario Perko, Henrik Arendrup.
Long-term outcome of lung transplantation for cystic fibrosis – Danish results.
European Journal of cardio-thoracic surgery. 26: 1180-1186.

21. Döring G., Høiby N. Consensus Study Group.
Early intervention and prevention of lung disease in cystic fibrosis: A European consensus.
J Cyst Fibros. 2004, 3: 67-91.

22. Skov M, Pandey JP, Pressler T, Høiby N, Koch C.
Immunoglobulin allotypes and IgG subclass antibody response to Aspergillus fumigatus in cystic fibrosis patients.
J Cystic Fibrosis 3, 2004; 173-178.

23. Skov M, McKay K, Koch C, Cooper P.J.
Prevalence of allergic broncho-pulmonary aspergillosis in cystic fibrosis in an area with a high frequency of atopy.
J of Cyst Fibr 2004; 3: 173-178.


11. Skov M, Main KM, Sillesen IB, Müller JR, Koch C, Thorsteinsson SL.
Binyrebarkinsufficiens efter kombineret behandling med itraconazol og budesonid.
Ugeskrift for Læger 2003;154 : 2198-202.

12. Stevens DA, Moss R, Kurup VP, Knutsen AP, Greenberger P,
Judson MA, Denning DW, Crameri R, Brody A, Light M, Skov M,
Maish W, Mastella G and the Cystic Fibrosis Foundation Consensus Conference.
Allergic bronchopulmonary aspergillosis in cystic  fibrosis – State of the Art: Cystic Fibrosis Foundation Consensus Conference.
Clin Infect Dis 2003; 37, Suppl 3: S225-64.

13. Jorgensen I.M., Johansen H.K., Frederiksen B., Pressler T., Hansen A.,
Vandamme P., Høiby N., Koch C. 
Epidemic spread of Pandoraea apista, a new pathogen causing severe lung disease in cystic fibrosis patients.
Pediatr Pulmonol. 2003; 36: 439-46.

14. Buchvald F, Eiberg H, Bisgaard H.
Heterogeneity of FeNO response to inhaled steroid in asthmatic children.
Clin Exp Allergy. 2003;33:1735-40.

15. Buchvald F, Bisgaard H. C
Comparisons of the complementary effect on exhaled nitric oxide of salmeterol vs montelukast in asthmatic children taking regular inhaled budesonide.
Ann Allergy Asthma Immunol. 2003;91:309-13.

16. H Bisgaard, M Hermansen, C Vrang, EA Andersen, G Dybmose, V Brændholt, K.G. Nielsen, E. Fog, L.V Pedersen, B. Smidth, B. Klug, J. Henriksen, M. Jørgensen, K Bønnelykke, D. Skoner, D Gentile.
A Randomized Trial of Montelukast in Respiratory Syncytial Virus Post-Bronchiolitis.
Am J Respir Crit Care Med 2003; 167:379–383.​


5. Kristensen K, Andersen EA, Andersen MH, Buchvald FF, Christensen H,
Heslet L, Bunk Lauritsen TL, Reveles RM, Sorgenfrei IF, Winther-Rasmussen S.
A three year population based survey of paediatric mechanical ventilation in east Denmark.
Dan Med Bull. 2002;49:67-9.

6. Garred P, Pressler T, Lanng S, Madsen HO, Moser C, Laursen I, Balstrup F,
Koch C, Koch C. 
Mannose-binding lectin (MBL) therapy in an  MBL-deficient patient with severe cystic fibrosis lung disease.
Pediatr Pulmonol. 2002 ;33:201-7.

7. Main KM, Skov M, Sillesen IB, Dige-Petersen H, Müller J, Koch C, Lanng S.
Cushing's syndrome due to pharmacological interaction in a cystic fibrosis patient.
Acta Paediatr. 2002;91:1008-11.

8. Skov M, Main KM, Sillesen IB, Müller J, Koch C, Lanng S.
Iatrogenic adrenal insufficiency as a side-effect of combined treatment of itraconazole and budesonide.
Eur Respir J. 2002 20:127-33.

9. Skov M, Høiby N, Koch C.
Itraconazole treatment of allergic bronchopulmonary aspergillosis in patients with cystic fibrosis.
Allergy. 2002 ;57:723-8.

10. Main KM, Skov M, Sillesen IB, Dige-Petersen H,
Lanng S, Müller J, Koch C.
Iatrogen Cushing´s syndrome in a cystic fibrosis patient due to the interaction between budesonide and itraconazole.
Acta Pæd. 2002; 91: 1008-11.​


1.Kim Gjerum Nielsen, H. Bisgaard.
Bronchodilation and bronchoprotection on asthmatic preschool children from formoterol administered by mechanically actuated dr​y-powder inhaler and spacer.
Am J Respir Crit Care Med 2001; 164: 256-259.

2. Kim Gjerum Nielsen, H. Bisgaard.
Discriminative capacity of bronchodilator response measured with three different lung function techniques in asthmatic and healthy children aged 2 to 5 years.
Am J Respir Crit Care Med 2001; 164: 554-559.

3. Anja Poulsen, Ann Kathrin Demeny,
Charlotte Bang Plum, Kim Gjerum Nielsen,
Kjeld Schmiegelow.
Pneumocystis Carinii pneumonia during maintenance treatment of childhood
acute lymphoblastic leukemia.
Med. Pediatr. Oncol. 2001;37:20-23.

4. Buchvald F, Bisgaard H.
FeNO measured at fixed exhalation flow rate during controlled tdal breathing in children from the age of 2 yr.
Am J Respir Crit Care Med. 2001, 699-704.​